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Incontinentia Pigmenti
MeSH HeadingIncontinentia Pigmenti
Tree NumberC16.131.077.445
Tree NumberC16.131.831.580
Tree NumberC16.320.850.420
Tree NumberC17.800.621.497
Tree NumberC17.800.804.580
Tree NumberC17.800.827.420
Annotationmultiple skin & other abnorm; do not confuse with INCONTINENTIA PIGMENTI ACHROMIANS see PIGMENTATION DISORDERS
Scope NoteA genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. Hyperpigmentation is bizarre and irregular. Sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Entry TermBloch-Sulzberger Syndrome
Allowable QualifiersBL CF CI CL CO DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RA RH RI RT SU TH UL UR US VE VI
Previous Indexing Pigmentation Disorders (1966-1986)
History Note91(87); was see under PIGMENTATION DISORDERS 1987-90
Date of Entry19860403
Unique IDD007184


MeSH Tree Structures

 
Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
   Congenital Abnormalities [C16.131]
      Abnormalities, Multiple [C16.131.077]
Alagille Syndrome [C16.131.077.065]
Angelman Syndrome [C16.131.077.095]
Bardet-Biedl Syndrome [C16.131.077.112]
Basal Cell Nevus Syndrome [C16.131.077.130]
Beckwith-Wiedemann Syndrome [C16.131.077.133]
Bloom Syndrome [C16.131.077.137]
Branchio-Oto-Renal Syndrome [C16.131.077.208]
Cockayne Syndrome [C16.131.077.250]
Cri-du-Chat Syndrome [C16.131.077.262]
De Lange Syndrome [C16.131.077.272]
Deaf-Blind Disorders [C16.131.077.299]  +
Down Syndrome [C16.131.077.327]
Ectodermal Dysplasia [C16.131.077.350]  +
Gardner Syndrome [C16.131.077.393]
Holoprosencephaly [C16.131.077.410]
Incontinentia Pigmenti [C16.131.077.445]
Laurence-Moon Syndrome [C16.131.077.509]
LEOPARD Syndrome [C16.131.077.525]
Marfan Syndrome [C16.131.077.550]
Mobius Syndrome [C16.131.077.578]
Nail-Patella Syndrome [C16.131.077.606]
Nevus Sebaceous of Jadassohn [C16.131.077.633]
Oculocerebrorenal Syndrome [C16.131.077.661]
Orofaciodigital Syndromes [C16.131.077.677]
Pallister-Hall Syndrome [C16.131.077.690]
POEMS Syndrome [C16.131.077.703]
Prader-Willi Syndrome [C16.131.077.730]
Proteus Syndrome [C16.131.077.740]
Prune Belly Syndrome [C16.131.077.745]
Rubella Syndrome, Congenital [C16.131.077.790]
Rubinstein-Taybi Syndrome [C16.131.077.804]
Short Rib-Polydactyly Syndrome [C16.131.077.850]
Smith-Lemli-Opitz Syndrome [C16.131.077.860]
Trichothiodystrophy Syndromes [C16.131.077.899]
Waardenburg's Syndrome [C16.131.077.938]
Wolf-Hirschhorn Syndrome [C16.131.077.944]
Wolfram Syndrome [C16.131.077.951]
Zellweger Syndrome [C16.131.077.970]

 
Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
   Congenital Abnormalities [C16.131]
      Skin Abnormalities [C16.131.831]
Acrodermatitis [C16.131.831.066]
Dyskeratosis Congenita [C16.131.831.150]
Ectodermal Dysplasia [C16.131.831.350]  +
Ehlers-Danlos Syndrome [C16.131.831.428]
Epidermolysis Bullosa [C16.131.831.493]  +
Ichthyosis [C16.131.831.512]  +
Incontinentia Pigmenti [C16.131.831.580]
Port-Wine Stain [C16.131.831.675]
Pseudoxanthoma Elasticum [C16.131.831.766]
Rothmund-Thomson Syndrome [C16.131.831.775]
Sclerema Neonatorum [C16.131.831.812]
Trichothiodystrophy Syndromes [C16.131.831.874]
Xeroderma Pigmentosum [C16.131.831.936]

 
Congenital, Hereditary, and Neonatal Diseases and Abnormalities [C16]
   Genetic Diseases, Inborn [C16.320]
      Skin Diseases, Genetic [C16.320.850]
Albinism [C16.320.850.080]  +
Cutis Laxa [C16.320.850.180]
Darier Disease [C16.320.850.190]
Dermatitis, Atopic [C16.320.850.210]
Dyskeratosis Congenita [C16.320.850.235]
Ectodermal Dysplasia [C16.320.850.250]  +
Ehlers-Danlos Syndrome [C16.320.850.260]
Epidermolysis Bullosa [C16.320.850.275]  +
Ichthyosiform Erythroderma, Congenital [C16.320.850.400]  +
Ichthyosis Bullosa of Siemens [C16.320.850.402]
Ichthyosis Vulgaris [C16.320.850.405]
Ichthyosis, X-Linked [C16.320.850.408]
Incontinentia Pigmenti [C16.320.850.420]
Keratoderma, Palmoplantar [C16.320.850.475]  +
Leukokeratosis, Hereditary Mucosal [C16.320.850.542]
Lipoid Proteinosis of Urbach and Wiethe [C16.320.850.595]
Pemphigus, Benign Familial [C16.320.850.700]
Porokeratosis [C16.320.850.730]
Porphyria, Erythropoietic [C16.320.850.738]
Porphyrias, Hepatic [C16.320.850.742]  +
Pseudoxanthoma Elasticum [C16.320.850.750]
Rothmund-Thomson Syndrome [C16.320.850.765]
Sjogren-Larsson Syndrome [C16.320.850.820]
Trichothiodystrophy Syndromes [C16.320.850.895]
Xeroderma Pigmentosum [C16.320.850.970]

 
Skin and Connective Tissue Diseases [C17]
   Skin Diseases [C17.800]
      Pigmentation Disorders [C17.800.621]
Argyria [C17.800.621.166]
Cafe-au-Lait Spots [C17.800.621.250]
Hyperpigmentation [C17.800.621.430]  +
Hypopigmentation [C17.800.621.440]  +
Incontinentia Pigmenti [C17.800.621.497]
Urticaria Pigmentosa [C17.800.621.893]
Xeroderma Pigmentosum [C17.800.621.936]

 
Skin and Connective Tissue Diseases [C17]
   Skin Diseases [C17.800]
      Skin Abnormalities [C17.800.804]
Acrodermatitis [C17.800.804.066]
Dyskeratosis Congenita [C17.800.804.150]
Ectodermal Dysplasia [C17.800.804.350]  +
Ehlers-Danlos Syndrome [C17.800.804.428]
Epidermolysis Bullosa [C17.800.804.493]  +
Ichthyosis [C17.800.804.512]  +
Incontinentia Pigmenti [C17.800.804.580]
Port-Wine Stain [C17.800.804.675]
Pseudoxanthoma Elasticum [C17.800.804.766]
Rothmund-Thomson Syndrome [C17.800.804.775]
Sclerema Neonatorum [C17.800.804.812]
Trichothiodystrophy Syndromes [C17.800.804.874]
Xeroderma Pigmentosum [C17.800.804.936]

 
Skin and Connective Tissue Diseases [C17]
   Skin Diseases [C17.800]
      Skin Diseases, Genetic [C17.800.827]
Albinism [C17.800.827.080]  +
Cutis Laxa [C17.800.827.180]
Darier Disease [C17.800.827.190]
Dermatitis, Atopic [C17.800.827.210]
Dyskeratosis Congenita [C17.800.827.235]
Ectodermal Dysplasia [C17.800.827.250]  +
Ehlers-Danlos Syndrome [C17.800.827.260]
Epidermolysis Bullosa [C17.800.827.275]  +
Ichthyosiform Erythroderma, Congenital [C17.800.827.400]  +
Ichthyosis Bullosa of Siemens [C17.800.827.403]
Ichthyosis Vulgaris [C17.800.827.405]
Ichthyosis, X-Linked [C17.800.827.408]
Incontinentia Pigmenti [C17.800.827.420]
Keratoderma, Palmoplantar [C17.800.827.475]  +
Leukokeratosis, Hereditary Mucosal [C17.800.827.595]
Muir-Torre Syndrome [C17.800.827.610]
Pemphigus, Benign Familial [C17.800.827.700]
Porokeratosis [C17.800.827.730]
Porphyria, Erythropoietic [C17.800.827.738]
Porphyrias, Hepatic [C17.800.827.742]  +
Pseudoxanthoma Elasticum [C17.800.827.750]
Rothmund-Thomson Syndrome [C17.800.827.775]
Sjogren-Larsson Syndrome [C17.800.827.820]
Trichothiodystrophy Syndromes [C17.800.827.895]
Xeroderma Pigmentosum [C17.800.827.970]

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