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Amelogenesis imperfecta

Amelogenesis imperfecta is a tooth development disorder in which the teeth are covered with thin, abnormally formed enamel.


Amelogenesis imperfecta is passed down through families as a dominant trait. That means you only need to get the abnormal gene from one parent in order for you to get the disease.


The enamel of the tooth is soft and thin. The teeth appear yellow and are easily damaged. Both baby teeth and permanent teeth are affected.

See also: Abnormal tooth color

Exams and Tests

A dentist can identify and diagnose the condition.


The treatment depends on the severity of the problem. Full crowns will improve the appearance of the teeth and protect them from damage. Eating a diet that is low in sugar and practicing very good oral hygiene can reduce the chance of developing cavities.

Outlook (Prognosis)

Treatment is often successful in protecting the teeth.

Possible Complications

The enamel is easily fractured and damaged, which affects the appearance of the teeth, especially if left untreated.

When to Contact a Medical Professional

Call your dentist if you have symptoms of this condition.

Update Date 2/25/2014

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